Notching in the posterior border of the ramus of mandible in a patient with neurofibromatosis type I - a case report.

نویسندگان

  • Bhuvana Krishnamoorthy
  • Parul Singh
  • Suma N Gundareddy
  • Manisha Lakhanpal Sharma
  • Manu Dhillon
چکیده

Neurofibromatosis Type I (NFI) is a relatively common hereditary, autosomal dominant neurocutaneous condition. It is a benign peripheral nerve sheath tumour arising from Schwann cells and peripheral fibroblasts. Even though it is a neurocutaneous disorder, NF I has significant skeletal manifestations. Oral and maxillofacial skeletal structures are also often involved in the form of deepening of sigmoid notch, enlarged mandibular canal and notching of inferior border of mandible. In this paper, we are reporting a female patient of NF I who presented with a notching in the posterior border of ascending ramus of mandible.

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عنوان ژورنال:
  • Journal of clinical and diagnostic research : JCDR

دوره 7 10  شماره 

صفحات  -

تاریخ انتشار 2013